

Recognizing and understanding this syndrome is important in knowing whom to test. This form of diabetes is non-ketotic, and patients do not have pancreatic autoantibodies. It usually manifests before 25 years of age.

Patients with this form of diabetes can sometimes be mistaken for having either type 1 diabetes (DM1) or type 2 diabetes mellitus (DM2).

MODY is the most common form of monogenic diabetes and exhibits autosomal dominant inheritance. In 1974, Tattersall and Fajans coined the term mature onset diabetes of the young (MODY).
